Ulcerative Fistulizing Ileitis Presenting a Diagnostic Dilemma between Crohn’s Disease and Intestinal Behçet’s Disease: A Case Report and Literature Review

N. Bouhdoud *

Hepato-Gastroenterology Department, University Hospital of Mohammed VI, Marrakesh, Morocco.

A. Sadik

Hepato-Gastroenterology Department, University Hospital of Mohammed VI, Marrakesh, Morocco.

F. Machayi

Hepato-Gastroenterology Department, University Hospital of Mohammed VI, Marrakesh, Morocco.

H. Aouroud

Hepato-Gastroenterology Department, University Hospital of Mohammed VI, Marrakesh, Morocco and Physiology Laboratory, Faculty of Medicine and Pharmacy, Cadi Ayyad University, Marrakech, Morocco.

O. Nacir

Hepato-Gastroenterology Department, University Hospital of Mohammed VI, Marrakesh, Morocco.

F. Lairani

Hepato-Gastroenterology Department, University Hospital of Mohammed VI, Marrakesh, Morocco.

A. Ait Errami

Hepato-Gastroenterology Department, University Hospital of Mohammed VI, Marrakesh, Morocco.

S. Oubaha

Hepato-Gastroenterology Department, University Hospital of Mohammed VI, Marrakesh, Morocco and Physiology Laboratory, Faculty of Medicine and Pharmacy, Cadi Ayyad University, Marrakech, Morocco.

Z. Samlani

Hepato-Gastroenterology Department, University Hospital of Mohammed VI, Marrakesh, Morocco.

K. Krati

Hepato-Gastroenterology Department, University Hospital of Mohammed VI, Marrakesh, Morocco.

*Author to whom correspondence should be addressed.


Abstract

Behçet’s disease is a rare systemic vasculitis that can affect the gastrointestinal tract. Intestinal involvement, or enteric Behçet’s disease, can mimic Crohn’s disease, making the differential diagnosis complex, particularly in chronic and fistulizing forms. We report the case of a 37-year-old man being treated for Behçet’s disease, presenting with ulcerative ileitis with pelvic fistulas, bilateral osteonecrosis of the femoral heads, and a prolonged course of the disease. Imaging findings and the lack of response to Behçet’s disease treatment led, following multidisciplinary consultation, to a diagnosis of Crohn’s disease. This case illustrates the diagnostic challenges posed by intestinal forms of Behçet’s disease that mimic chronic inflammatory bowel disease.

Keywords: Behçet's disease, Crohn's disease, enteropathology associated with Behçet's disease, ulcerative ileitis, gastrointestinal fistulas, differential diagnosis


How to Cite

Bouhdoud, N., A. Sadik, F. Machayi, H. Aouroud, O. Nacir, F. Lairani, A. Ait Errami, S. Oubaha, Z. Samlani, and K. Krati. 2026. “Ulcerative Fistulizing Ileitis Presenting a Diagnostic Dilemma Between Crohn’s Disease and Intestinal Behçet’s Disease: A Case Report and Literature Review”. International Research Journal of Gastroenterology and Hepatology 9 (1):192-97. https://doi.org/10.9734/irjgh/2026/v9i1151.

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